Lian Nengjing; Zhu Xiaonong; Lan Baosen; et al(Institute of Otorhinolaryngology,Beijing, 100005 )
Mondini's deafness was the congenital malformation of inner ear. We studied 199 ears of 106 cases. Most of them were found deaf when they were babies. High resolution computed tomography of temperal bone was described:cochlea malformation 4 ears;malformation of cochlea, vestibule and semicircular canal 90 ears; vestibule of semicircular malformation without cochlea rnalformation 1 05 ears,this type was called the vestibule malformation or untypically Mondini's. Of all the 199 ears there were 81 ears with enlagement of the vestibule aqueducts. The pathogeny,cli-nical manifestation and treatment were discussed.